Compromised lipid metabolism, mitochondria respiration and neuroprotective effects in iPSC-derived astrocytes from a Smith-Lemli-Opitz syndrome patient. uri icon

authors

  • Kawatani, Keiji
  • Kanekiyo, Takahisa
  • Baker, Samantha K
  • Yaeger, Jazmine D W
  • Anderson, Ruthellen H
  • Ren, Yingxue
  • Li, Zonghua
  • Bao, Hanmei
  • Han, Xianlin
  • Francis, Kevin R

publication date

  • November 18, 2025